2010 Future treatment strategies in phenylketonuria

Phenylketonuria (McKusick 261600, PKU) is one of the best- ..... growth advantage over native hepatocytes [66]. .... S. Yannicelli, R.H. Singh, L.J. E...

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Jun 21, 2017 - causing blood phenylalanine concentrationsto increase sometimes to levels above 3000 iimol/l and phenylketones to appear in the urine.

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In screened and treated. Abadie V. Maternal phenylketonuria. Orphanet encyclopedia, January 2004. http://www.orpha.net/data/patho/GB/uk-PKU.pdf. 2 ...

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